KEY FACTS
Terminology
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Failure of kidneys to form
Imaging
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No kidneys in renal fossa or anywhere else in fetus
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Adrenal glands are present and large, can mimic kidneys
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Have ice cream sandwich appearance with hypoechoic cortex and hyperechoic medulla
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Flattened, lying down appearance; lacks normal tricorn hat configuration
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Absent renal arteries
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Best evaluated with coronal aorta color Doppler view
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No fluid-filled bladder
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Best evaluated with axial pelvis color Doppler view showing no bladder between umbilical arteries
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No amniotic fluid in 2nd/3rd trimester (anhydramnios)
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Normal or low-normal fluid might be seen before 16 wk
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Associated findings
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Pulmonary hypoplasia from oligohydramnios
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Limb deformities: Club feet, contractures
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Facial anomalies: Micrognathia, low-set ears
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Top Differential Diagnoses
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Other causes of severe oligohydramnios
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Premature rupture of membranes
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Severe growth restriction
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Bilateral renal anomaly
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Clinical Issues
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Bilateral agenesis is considered lethal anomaly
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Associated with aneuploidy and genetic syndromes
Scanning Tips
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Saline infusion may help with fetal anatomy evaluation
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Set color Doppler gain carefully so as not to “light up” lumbar arteries, which may mimic renal arteries
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Look for pelvic kidney when kidneys not seen in renal fossa
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Renal artery may come off iliac artery
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