Posterior Urethral Valves





KEY FACTS


Imaging





  • Exclusively in male fetuses



  • Bladder often grossly dilated, filling entire abdomen and increasing abdominal circumference



  • Distended bladder “funnels” into urethra




    • Keyhole sign from dilated posterior urethra




  • Small, bell-shaped chest



  • Hydronephrosis/hydroureter



  • Rupture → urinoma or urinary ascites



  • Oligohydramnios or anhydramnios in severe cases



  • Kidneys may show signs of obstructive renal dysplasia



Top Differential Diagnoses





  • Cloacal malformation seen exclusively in females




    • Dilated, fluid-filled vagina can mimic bladder




  • Prune-belly syndrome



Clinical Issues





  • Most common cause of fetal lower urinary tract obstruction



  • Variable degree of fetal renal damage, directly affects long-term outcomes and survival (overall mortality: 25-50%)



  • May tap fetal bladder and assess urine electrolytes




    • Intervention (e.g., vesicoamniotic shunt) may be considered in cases with good prognostic markers




Scanning Tips





  • If bladder appears large, check several times during exam to see if it decompresses




    • Likely normal if otherwise normal urinary tract and normal amniotic fluid




  • Determine sex




    • May be difficult in setting of oligohydramnios



    • If female, what appears to be a dilated bladder may actually be vagina




  • Obtain focused images of bladder base to evaluate for dilation of posterior urethra (keyhole)



  • Evaluate kidneys for signs of renal parenchymal damage




    • Increased echogenicity, small cortical cysts, atrophy








Sagittal graphic shows the bladder funneling into a dilated posterior urethra . The valve forms a thin membrane , blocking antegrade flow of urine and creating a lower urinary tract obstruction (LUTO).








US at 15 weeks shows gross distention of the bladder , with severe oligohydramnios and a small, bell-shaped chest . The inset shows dilatation of the posterior urethra , the keyhole sign. This is the “key” to the diagnosis and differentiates posterior urethral valves from other causes of LUTO.

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Nov 10, 2024 | Posted by in ULTRASONOGRAPHY | Comments Off on Posterior Urethral Valves

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