KEY FACTS
Imaging
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Exophytic mixed cystic/solid mass extending from sacrum
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Variable size but often large, with potential for extremely rapid growth
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Commonly extends into pelvis and abdomen
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Solid tumors may have significant arteriovenous shunting
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Color Doppler essential to evaluate vascularity
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Scan every 1-3 weeks depending on size, vascularity, impending hydrops, and complications
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Calculate tumor volume:fetal weight ratio (TFR)
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Tumor volume: Tumor length x width x depth x 0.523
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Divide by estimated fetal weight
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TFR > 0.12 prior to 24 weeks has poor prognosis
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Top Differential Diagnoses
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Myelomeningocele in differential for cystic SCGT
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Sac contains meninges + neural elements
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Splayed posterior spinal ossification centers
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Chiari 2 malformation of brain
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Clinical Issues
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Large, solid, vascular tumors have high mortality and morbidity; better outcome for cystic tumors
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Prognosis significantly worse for fetus than neonate
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Fetal diagnosis 30-50% mortality
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Scanning Tips
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Carefully assess for intrapelvic extension as it is part of surgical classification
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Try to measure tumor in same plane each time
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Evaluate for signs of impending cardiovascular compromise
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Tumor growth, amniotic fluid index, placental thickness
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Any signs of developing hydrops (skin edema, pleural or pericardial effusion, ascites)
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Early vascular signs of high cardiac output state
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Increased cardiothoracic ratio (> 50%)
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Inferior cava diameter > 1 cm
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Increase descending aortic velocity (> 120 cm/s)
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Look for complications: Tumor rupture/hemorrhage