Clinical Presentation

Severe cyanosis in a newborn.

Frontal chest radiograph demonstrates massive “boxlike” cardiomegaly with marked convexity of the right border of the heart (arrow). Pulmonary vascularity appears to be diminished.

Differential Diagnosis

• Ebstein anomaly (EA): Massive cardiomegaly with marked convexity of the right border of the heart, as well as diminished pulmonary vascularity, is typical of EA.