CASE 38
Used with permission from McGahan JP, et al: Fetal Heart. In McGahan JP, Goldberg BB [eds]: Diagnostic Ultrasound, 2nd ed. New York: Informa Healthcare USA, 2008; 1275.
History: A patient with a fetal cardiac abnormality identified on an ultrasound scan performed at an outside institution is referred for a level II examination.
1. What should be included in the differential diagnosis? (Choose all that apply.)
C. Hypoplastic left heart syndrome (HLHS)
2. Which of the following is not a feature of HLHS?
B. Hypoplasia of the ascending aorta
C. Small mitral valve with poor mitral valve motion
D. Small aortic valve and aortic valve motion
3. Which of the following is not an anomaly associated with HLHS?
B. High frequency of extracardiac malformation
C. Increased risk of chromosomal abnormalities
4. Which of the following statements concerning HLHS is false?
A. HLHS is associated with greater than 50% death rate in utero.
B. HLHS is the most common cardiac cause of death within the first month of life.