Dermatofibrosarcoma Protuberans
KEY FACTS
Terminology
Imaging
- • Nearly always arising from dermis, then infiltrates subcutaneous tissue
- • Protruding mass arising from skin with bluish or reddish discoloration
- • Well-marginated, hypoechoic subcutaneous mass with posterior enhancement
- • Color Doppler imaging findings very variable
- • US helps to characterize tumor type as well as assess local infiltration
Clinical Issues
- • Slowly growing, slowly evolving cutaneous mass
- • Starts as small nodule, grows into medium erythematous or bluish lesion
- • Cutaneous ulceration and satellite nodules in advanced lesions
- • Occasionally, plaque-like indurated region progressing to single or multiple protuberant nodules
- • Locally infiltrative
- • Uncommonly metastasize (3-5%)
with bluish discoloration on the dorsum of the 2nd toe is shown. The mass had been growing slowly for 3 years.
within the subcutaneous tissues in contact with the dermis. The mass contacts the extensor digitorum tendon 
over the proximal phalanx 
. The tendon moved freely on dynamic examination.
. This level of hyperemia is unusually high for dermatofibrosarcoma protuberans (DFSP).
in contact with but separate from the extensor tendon 
overlying the proximal phalanx. Histology revealed DFSP.
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