Bladder Exstrophy





KEY FACTS


Terminology




  • •

    Failure of closure of lower abdominal wall resulting in exposed bladder



Imaging




  • •

    Inability to demonstrate fluid-filled bladder


  • •

    Soft tissue mass/nodular contour of lower anterior abdominal wall due to exposed posterior bladder wall


  • •

    Normal fluid



Top Differential Diagnoses




  • •

    Absent bladder



    • ○

      Renal anomalies or other conditions with low/absent urine production are associated with oligo/anhydramnios


    • ○

      If associated with oligohydramnios in monochorionic twin, may indicate twin-twin transfusion syndrome



  • •

    Cloacal exstrophy



    • ○

      Absent fluid-filled bladder, imperforate anus


    • ○

      Bowel herniation through abdominal wall defect → elephant trunk sign




Scanning Tips




  • •

    Red flag for this diagnosis is normal amniotic fluid without visible bladder



    • ○

      Obtain midline sagittal image through torso for abdominal wall contour


    • ○

      Check cord insertion site; inferiorly displaced in bladder exstrophy


    • ○

      Evaluate for genital anomalies, which are common in both males and females


    • ○

      Look for anal dimple on axial image of perineum



  • •

    Do not confuse cystic pelvic structures with bladder



    • ○

      Normal bladder fills and empties repeatedly during scan


    • ○

      Umbilical arteries encompass bladder as they course from internal iliac arteries to umbilicus



  • •

    Use 3D surface-rendered ultrasound images to clarify anatomy







Axial oblique US shows the umbilical arteries . The bladder, normally seen as a fluid-filled structure between them, was never visible in this case, even though the kidneys and amniotic fluid volume were normal. The spine is shown for orientation.





Nov 10, 2024 | Posted by in ULTRASONOGRAPHY | Comments Off on Bladder Exstrophy

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