Developmental dysplasia of the hip
Fig. 5.20a–c
Fig. 5.21, p. 508 |
Hypoplastic acetabular roof with later development of increasing sclerosis. Posterosuperior dislocation of the femoral head ± flattening of the femoral head. |
Ultrasound (US) is the screening modality of choice before ossification excludes visualization of the hip structures (below the age of 6 mo). |
Secondary hip dysplasia |
Increased acetabular angle. Shallow acetabulum. Coxa valga, ± femoral head dislocation and flattening. |
Generally occurs in neuromuscular diseases with spasticity of the lower extremities. May develop in a previously normal hip. |
Arthrogryposis |
Very thin diaphyses, osteopenia, dislocation and subluxation of large joints. |
Joint contractures and decreased muscle bulk. |
Ehlers-Danlos syndrome types III and VII |
Hip dislocation with an otherwise normal appearing skeleton. |
Calcified round areas of subcutaneous fat necrosis. |
Campomelic dysplasia
Fig. 5.14, p. 501 |
(see Table 5.12 ) |
|
Larsen syndrome |
Accessory carpal ossification centers, double calcaneal ossification center. Dislocation of large joints. |
Flat facies. Clinical DD: Marfan syndrome, arthrogryposis, and Ehlers-Danlos syndrome. |