63 Von Hippel-Lindau Disease

CASE 63


Clinical Presentation


Routine follow-up study in an asymptomatic patient with known von Hippel-Lindau disease.




image

Fig. 63.1 (A) Postcontrast CT image shows bilateral renal cysts. There is a large cyst within the right kidney with thick enhancing septations (arrowhead). Note the multiple pancreatic cysts (arrow). (B) Axial image shows a mixed solid and cystic lesion in the left kidney (arrowhead), along with an enhancing nodule in the chord (arrow). (C)An additional complex cyst with enhancing septation is seen in the right kidney (arrowhead), along with a small enhancing lesion in the left kidney (arrowhead).


Radiologic Findings


Postcontrast computed tomography (CT) images demonstrate bilateral multiple low-attenuation renal cysts, some of which show enhancing nodules or septations or have solid components (Fig. 63.1). There is also an enhancing lesion within the spinal cord, as well as multiple cysts seen in the pancreatic head.


Diagnosis


Von Hippel-Lindau disease


Differential Diagnosis



  • Autosomal dominant polycystic kidney disease
  • Tuberous sclerosis
  • Acquired cystic disease of dialysis

Discussion

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4 Hydatid Disease 33 Islet Cell Tumor of the Pancreas (Insulinoma) 60 Renal Changes from Lithium Toxicity 100 Gossypiboma (Textiloma or Retained Surgical Sponge) 149 Tuberculous Epididymo-Orchitis 141 Mature Cystic Teratoma (Dermoid Cyst)

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Dec 26, 2015 | Posted by in GASTROINTESTINAL IMAGING | Comments Off on 63 Von Hippel-Lindau Disease

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