Subgroups
Risk markers
Recommendations
Follow-up
ICD indication
Definite ARVC: high risk
Aborted SD
Reduce physical exercise
Annually, including:
Recommended
Sustained VT
Avoid competitive sport
Electrocardiography
Unexplained syncope
β-blockers
Cardiac imaging (echocardiography vs. CMR)
Holter
Exercise stress testing
Definite ARVC: moderate risk
Extensive disease (severe RV dysfunction, large LV involvement)
Reduce physical exercise
Annually including:
Consider
Nonsustained VT
Avoid competitive sport
Electrocardiography
β-blockers
Cardiac imaging (echocardiography vs. CMR)
Holter
Exercise stress testing
Definite ARVC: low risk
Remaining patients with definite diagnosis of ARVC
Reduce physical exercise
Annually including:
Not recommended
Avoid competitive sport
Electrocardiography
β-blockers
Cardiac imaging (echocardiography vs. CMR)
Holter
Exercise stress testing
Asymptomatic mutation carriers
Asymptomatic mutation-carrying relatives of ARVC
Reduce physical exercise
Annually including:
Not recommended
Avoid competitive sport
Electrocardiography
Cardiac imaging (echocardiography vs. CMR)
Holter
Exercise stress testing
References
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