Chapter 151 Plexiform neurofibromas may involve the parapharyngeal space (PPS). PPS neurofibromas typically occur in patients with neurofibromatosis type 1 (NF type 1). Patients with nerofibromas of the PPS typically have known neurofibromatosis and have associated findings. The involvement of the PPS is due to involvement of branches of small nerves that traverse the PPS. Rarely do patients present with findings associated with PPS masses as the only symptoms. Neurofibromas are composed of enlarged neurofibrils, whereas schwannomas are composed of enlarged Schwann’s cells. Schwannomas are encapsulated tumors and are easier to resect from the involved nerve. Neurofibromas are difficult to resect because they arise from intrinsic components of the nerve. Because NF type 1 may involve multiple sites and structures and neurofibromas are difficult to resect, surgery is warranted only if there are symptoms and significant compression of vital structures or if there is a suspicion of malignant degeneration.
Neurofibroma
Epidemiology
Clinical Findings
Pathology
Treatment
Imaging Findings (Fig. 151–1)
CT
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