• Up to 4 types have been described: • Recto-urethral fistula: this rare abnormality is usually associated with an imperforate anus • Urethral duplication: there is usually complete duplication with one of the urethras ending as a hypospadias • Hypospadias: absence of the ventral aspect of the distal urethra • Epispadias: absence of the dorsal aspect of the distal urethra
Urethra
URETHRA: BENIGN DISORDERS
CONGENITAL ANOMALIES
Clinical presentation
Type 1 (the most common): two mucosal folds at the level of the verumontanum with a ventral central slit-like orifice
Type 3: this has a pin-point, eccentric orifice which results in forward ballooning of the valve, giving a ‘wind in the sail’ appearance on an oblique MCUG projection
there is a high association with renal dysplasia and minimal upper tract dilatation
Other urethral anomalies
air within the bladder confirms the diagnosis
Urethra
incomplete obliteration may lead to the formation of cysts between the bladder and rectum which can present with urinary frequency or obstructive symptoms
it is often associated with maldevelopment of the genitalia
they are located near the distal verumontanum and result from the abnormal migration of mucosal folds (Wolffian duct remnants) from the verumontanum to the membranous urethra
progressive oligohydramnios during pregnancy (± pulmonary hypoplasia)
obstructive symptoms
infection
haematuria
there may be dilatation of the posterior uretha proximal to the valve
vesicoureteric reflux may be present (and is associated with poor renal function on the affected side)
infection
carcinoma
increased urinary frequency
dysuria
dyspareunia
it usually has a short neck
Ureaplasma urealyticum
tuberculosis
schistosomiasis
strictures
reflux into the glands of Littre, Cowper’s gland ducts, prostatic ducts and seminal vesicles
pseudodiverticulae
there is proximal dilatation and it classically follows a gonococcal urethritis




