19 Tracheobronchomegaly: Mounier-Kuhn Syndrome

CASE 19


image Clinical Presentation


38-year-old woman with recurrent respiratory infections


image Radiologic Findings


Coned-down PA (Fig. 19.1A) and lateral (Fig. 19.1B) chest radiographs demonstrate enlargement of the tracheal lumen and bilateral central thin-walled pulmonary cystic lesions. HRCT (lung window) (Figs. 19.1C, 19.1D) demonstrates marked tracheal enlargement involving the origins of the mainstem bronchi. Note the corrugated contour of the tracheal wall and bilateral branching thin-walled cystic lesions located centrally in the lung, consistent with bronchiectasis.



image


Fig. 19.1


image Diagnosis


Tracheobronchomegaly; Mounier-Kuhn Syndrome


image Differential Diagnosis


• Bronchiectasis


• Williams-Campbell Syndrome


• Chronic Airway Inflammation/Infection with Tracheobronchomalacia


• Allergic Bronchopulmonary Fungal Disease


image Discussion


Background


Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare condition also known as tracheal diverticulosis and tracheobronchiectasis.


Etiology


The etiology of tracheobronchomegaly is unknown. Some authors have postulated a congenital etiology

Jan 14, 2016 | Posted by in RESPIRATORY IMAGING | Comments Off on 19 Tracheobronchomegaly: Mounier-Kuhn Syndrome
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