Complete agenesis: Complete absence of pancreatic neck, body, and tail, Santorini duct, and minor papilla
–
Ventral pancreas (head and uncinate) appears normal
–
MRCP: Visualization only of short ventral duct, with absence of accessory and dorsal duct system
Partial agenesis: Variable appearance of pancreatic body (depending on degree of agenesis), with small remnant Santorini duct and minor papilla
–
Pancreas may appear short or truncated with normal pancreatic head and rounded upstream margin
•
ERCP
Complete agenesis: Filling of short ventral duct without identifiable dorsal ducts or minor papilla
Partial agenesis: Main pancreatic duct is shortened, some dorsal ducts remain with filling of atretic Santorini duct
TOP DIFFERENTIAL DIAGNOSES
•
Pancreatic ductal carcinoma
•
Chronic pancreatitis (pseudoagenesis)
•
Post-traumatic pancreatic atrophy
