Mucinous cystadenocarcinoma (90%)
Colonic-type adenocarcinoma (10%)
Lymphoma (< 1%)
Carcinoid (common, usually incidental at appendectomy)
IMAGING
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Round or oval, cystic or solid, mass near tip of cecum
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Mucocele
RLQ soft tissue mass with curvilinear mural calcification on radiography is highly suggestive
Ovoid cystic mass ± internal echoes (septations) on US
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Mucinous tumor: RLQ cystic mass, usually > 2 cm
Mucinous type has strong propensity to form mucocele
May have curvilinear calcification in wall
Mucinous cystadenocarcinoma is most common cause of pseudomyxoma peritonei