Sagittal T1WI MR shows multiple areas of ↓ signal in multiple vertebral bodies without paraspinal or epidural soft tissue. Compression fractures are present at multiple levels , some with normal marrow due to old lesions .
Sagittal STIR MR shows increased signal lesions within multiple vertebral bodies. Multiple pathologic compression fractures are present. Intervening disc signal is normal, and there is no paraspinal abnormality.
• Autosomal recessive syndromic form of disease is Majeed syndrome (OMIM 609628)
Definitions
• Autoinflammatory disorder of bone with fever, multifocal painful nonpyogenic bone lesions, relapsing and remitting course in children and adolescents