Mayer-Rokitansky-Kuster-Hauser syndrome. Twenty-year-old woman with amenorrhea. (1) Absence of vagina. (a) MR sagittal T2 on the midline displays absence of vagina almost until the introitus, with adipose tissue between two hypointense lines very likely representing the rectovaginal septum (long horizontal arrow) and the vesicovaginal septum (short horizontal arrow). The lower vagina (LV) is present with a cone shape and an apex (oblique arrow) representing the junction with the remnant upper two-thirds vagina. (b–c). Axial T2 at two levels. Through the middle part of the posterior wall of the bladder (b) allows to definitely confirming the absence of vagina until the introitus; At the level of the posterior and inferior part of the pubis (c) displays a normal vestibular vagina. (2) Uterine and tubal remnants. (d, e). Sagittal T2 through the midline (d) displays between the upper part of the bladder and rectum low intensity tissue (arrow). Axial T2 through this tissular mass (e) shows a central mass (central arrow) with irregular borders related to a remnant of the uterus and laterally two tubular structures with a hyperintense to intermediate signal related to tubal remnants (lateral arrow). (f, i). DMR without injection (f) at the arterial (g), venous (h), and late (i) phases. At the arterial phase (g), tubal arterial vessels are displayed in the tubal remnants. At the venous phase (h) and even better on the delayed (i), a significant contrast uptake is visualized in the uterus and tubes remnants, with a characteristic fold appearance in the right tube at the venous phase. (3) Normal ovaries are visualized on axial T2 (j)