Pulmonary Hypertension

34 Pulmonary Hypertension


With Anne Geoffray


Definition and Classification
















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Jan 14, 2016 | Posted by in RESPIRATORY IMAGING | Comments Off on Pulmonary Hypertension

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Table 34.1 World Health Organization Classification of Pulmonary Arterial Hypertension
1. Pulmonary arterial hypertension

  • 1.1. Idiopathic
  • 1.2. Familial
  • 1.3. Associated with:

    • 1.3.1. Connective tissue disease
    • 1.3.2. Congenital systemic pulmonary shunts
    • 1.3.3. Portal hypertension
    • 1.3.4. Human immunodeficiency virus (HIV) infection
    • 1.3.5. Drugs and toxins
    • 1.3.6. Others (thyroid disorders, glycogen storage disease, Gaucher’s disease, hereditary hemorrhagic telangiectasia, hemoglobulinopathies, myeloproliferative disorders, splenectomy)

  • 1.4. Associated with significant venous or capillary involvement

    • 1.4.1. Pulmonary veno-occlusive disease
    • 1.4.2. Pulmonary capillary hemangiomatosis

  • 1.5. Persistent pulmonary hypertension of the newborn
2. Pulmonary hypertension associated with left-heart diseases

  • 2.1. Left-sided atrial or ventricular heart disease
  • 2.2. Left-sided valvular heart disease
3. Pulmonary hypertension associated with lung respiratory diseases and/or hypoxemia